Chapter 3: Diseases of the blood and blood-forming organs
151 billable codes (3-4 characters)
D50.0 Iron deficiency anemia secondary to blood loss (chronic) D50.1 Sideropenic dysphagia D50.8 Other iron deficiency anemias D50.9 Iron deficiency anemia, unspecified D51.0 Vitamin B12 defic anemia due to intrinsic factor deficiency D51.1 Vit B12 defic anemia d/t slctv vit B12 malabsorp w protein D51.2 Transcobalamin II deficiency D51.3 Other dietary vitamin B12 deficiency anemia D51.8 Other vitamin B12 deficiency anemias D51.9 Vitamin B12 deficiency anemia, unspecified D52.0 Dietary folate deficiency anemia D52.1 Drug-induced folate deficiency anemia D52.8 Other folate deficiency anemias D52.9 Folate deficiency anemia, unspecified D53.0 Protein deficiency anemia D53.1 Other megaloblastic anemias, not elsewhere classified D53.2 Scorbutic anemia D53.8 Other specified nutritional anemias D53.9 Nutritional anemia, unspecified D55.0 Anemia due to glucose-6-phosphate dehydrogenase deficiency D55.1 Anemia due to other disorders of glutathione metabolism D55.3 Anemia due to disorders of nucleotide metabolism D55.8 Other anemias due to enzyme disorders D55.9 Anemia due to enzyme disorder, unspecified D56.0 Alpha thalassemia D56.1 Beta thalassemia D56.2 Delta-beta thalassemia D56.3 Thalassemia minor D56.4 Hereditary persistence of fetal hemoglobin [HPFH] D56.5 Hemoglobin E-beta thalassemia D56.8 Other thalassemias D56.9 Thalassemia, unspecified D57.1 Sickle-cell disease without crisis D57.3 Sickle-cell trait D58.0 Hereditary spherocytosis D58.1 Hereditary elliptocytosis D58.2 Other hemoglobinopathies D58.8 Other specified hereditary hemolytic anemias D58.9 Hereditary hemolytic anemia, unspecified D59.0 Drug-induced autoimmune hemolytic anemia D59.2 Drug-induced nonautoimmune hemolytic anemia D59.4 Other nonautoimmune hemolytic anemias D59.5 Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli] D59.6 Hemoglobinuria due to hemolysis from other external causes D59.8 Other acquired hemolytic anemias D59.9 Acquired hemolytic anemia, unspecified D60.0 Chronic acquired pure red cell aplasia D60.1 Transient acquired pure red cell aplasia D60.8 Other acquired pure red cell aplasias D60.9 Acquired pure red cell aplasia, unspecified D61.1 Drug-induced aplastic anemia D61.2 Aplastic anemia due to other external agents D61.3 Idiopathic aplastic anemia D61.9 Aplastic anemia, unspecified D62 Acute posthemorrhagic anemia D63.0 Anemia in neoplastic disease D63.1 Anemia in chronic kidney disease D63.8 Anemia in other chronic diseases classified elsewhere D64.0 Hereditary sideroblastic anemia D64.1 Secondary sideroblastic anemia due to disease D64.2 Secondary sideroblastic anemia due to drugs and toxins D64.3 Other sideroblastic anemias D64.4 Congenital dyserythropoietic anemia D64.9 Anemia, unspecified D65 Disseminated intravascular coagulation D66 Hereditary factor VIII deficiency D67 Hereditary factor IX deficiency D68.1 Hereditary factor XI deficiency D68.2 Hereditary deficiency of other clotting factors D68.4 Acquired coagulation factor deficiency D68.8 Other specified coagulation defects D68.9 Coagulation defect, unspecified D69.0 Allergic purpura D69.2 Other nonthrombocytopenic purpura D69.3 Immune thrombocytopenic purpura D69.6 Thrombocytopenia, unspecified D69.8 Other specified hemorrhagic conditions D69.9 Hemorrhagic condition, unspecified D70.0 Congenital agranulocytosis D70.1 Agranulocytosis secondary to cancer chemotherapy D70.2 Other drug-induced agranulocytosis D70.3 Neutropenia due to infection D70.4 Cyclic neutropenia D70.8 Other neutropenia D70.9 Neutropenia, unspecified D71.1 Leukocyte adhesion deficiency D71.8 Other functional disorders of polymorphonuclear neutrophils D71.9 Functional disorders of polymorphonuclear neutrophils, unsp D72.0 Genetic anomalies of leukocytes D72.9 Disorder of white blood cells, unspecified D73.0 Hyposplenism D73.1 Hypersplenism D73.2 Chronic congestive splenomegaly D73.3 Abscess of spleen D73.4 Cyst of spleen D73.5 Infarction of spleen D73.9 Disease of spleen, unspecified D74.0 Congenital methemoglobinemia D74.8 Other methemoglobinemias D74.9 Methemoglobinemia, unspecified D75.0 Familial erythrocytosis D75.1 Secondary polycythemia D75.9 Disease of blood and blood-forming organs, unspecified D75.A Glucose-6-phosphate dehydrgnse (G6PD) defic without anemia D76.1 Hemophagocytic lymphohistiocytosis D76.2 Hemophagocytic syndrome, infection-associated D76.3 Other histiocytosis syndromes D77 Oth disord of bld/bld-frm organs in diseases classd elswhr D80.0 Hereditary hypogammaglobulinemia D80.1 Nonfamilial hypogammaglobulinemia D80.2 Selective deficiency of immunoglobulin A [IgA] D80.3 Selective deficiency of immunoglobulin G [IgG] subclasses D80.4 Selective deficiency of immunoglobulin M [IgM] D80.5 Immunodeficiency with increased immunoglobulin M [IgM] D80.6 Antibody defic w near-norm immunoglob or w hyperimmunoglob D80.7 Transient hypogammaglobulinemia of infancy D80.8 Other immunodeficiencies with predominantly antibody defects D80.9 Immunodeficiency with predominantly antibody defects, unsp D81.0 Severe combined immunodeficiency with reticular dysgenesis D81.1 Severe combined immunodeficiency w low T- and B-cell numbers D81.2 Severe combined immunodef w low or normal B-cell numbers D81.4 Nezelof's syndrome D81.5 Purine nucleoside phosphorylase [PNP] deficiency D81.6 Major histocompatibility complex class I deficiency D81.7 Major histocompatibility complex class II deficiency D81.9 Combined immunodeficiency, unspecified D82.0 Wiskott-Aldrich syndrome D82.1 Di George's syndrome D82.2 Immunodeficiency with short-limbed stature D82.3 Immunodef fol heredit defctv response to Epstein-Barr virus D82.4 Hyperimmunoglobulin E [IgE] syndrome D82.8 Immunodeficiency associated with oth major defects D82.9 Immunodeficiency associated with major defect, unspecified D83.0 Com variab immunodef w predom abnlt of B-cell nums & functn D83.1 Com variab immunodef w predom immunoreg T-cell disorders D83.2 Common variable immunodef w autoantibodies to B- or T-cells D83.8 Other common variable immunodeficiencies D83.9 Common variable immunodeficiency, unspecified D84.0 Lymphocyte function antigen-1 [LFA-1] defect D84.1 Defects in the complement system D84.9 Immunodeficiency, unspecified D86.0 Sarcoidosis of lung D86.1 Sarcoidosis of lymph nodes D86.2 Sarcoidosis of lung with sarcoidosis of lymph nodes D86.3 Sarcoidosis of skin D86.9 Sarcoidosis, unspecified D89.0 Polyclonal hypergammaglobulinemia D89.1 Cryoglobulinemia D89.2 Hypergammaglobulinemia, unspecified D89.3 Immune reconstitution syndrome D89.9 Disorder involving the immune mechanism, unspecified